Orbital IgG4-associated diseases
نویسندگان
چکیده
منابع مشابه
IgG4-associated orbital and ocular inflammation
BACKGROUND IgG4-associated orbital and ocular inflammation is a relatively unknown entity characterized by sclerosing inflammation with infiltration of IgG4-positive plasma cells. Some so-called idiopathic inflammation syndromes are being re-classified as IgG4-associated inflammation with histopathologic evaluation. FINDINGS We report three cases with differing manifestations of IgG4-associat...
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Dear Editor, IgG4-related disease (RD) is a systemic immune-mediated syndrome characterized by mass-forming lesions in one or more exocrine glands or other extranodal sites caused by lymphoplasmacytic infiltrates and sclerosis. Certain autoimmune diseases and inflammatory disorders, such as rheumatoid arthritis, Hashimoto's thyroiditis, and Sjögren's syndrome, have been shown to be associated w...
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IgG4-related disease (IgG4-RD) is a potentially multiorgan disorder. In this study, clinical and serological features from 132 IgG4-RD patients were compared about organ correlations. Underlying pathologies comprised autoimmune pancreatitis (AIP) in 85 cases, IgG4-related sclerosing cholangitis (IgG4-SC) in 12, IgG4-related sialadenitis (IgG4-SIA) in 56, IgG4-related dacryoadenitis (IgG4-DAC) i...
متن کاملOrbital IgG4-Related Disease: Clinical Features and Diagnosis
Orbital IgG4-related disease, which can occur in adults of any age, is characterized by IgG4-positive lymphoplasmacytic infiltrations in ocular adnexal tissues. The signs and symptoms include chronic noninflammatory lid swelling and proptosis. Patients often have a history of allergic disease and elevated serum levels of IgG4 and IgE as well as hypergammaglobulinemia. Orbital IgG4-related disea...
متن کاملAutoimmune pancreatitis and IgG4-related systemic diseases.
Autoimmune pancreatitis (AIP) is a rare form of chronic pancreatitis that is characterized by lymphoplasmacytic infiltrate, storiform fibrosis, obliterative phlebitis, and increased IgG4(+) plasma cells. Serum IgG4 levels usually are elevated. Patients with AIP frequently have disease affecting other organs or sites; these tissues show similar histologic changes, including increased IgG4(+) pla...
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ژورنال
عنوان ژورنال: Pathology Discovery
سال: 2017
ISSN: 2052-7896
DOI: 10.7243/2052-7896-5-4